Abstract: Erdheim-Chester Disease（ ECD） is a rare histiocytic tumor. The disease is characterized by the symptom of bone pain of the whole body. We report a case of BRAF V600E-positive ECD related tumor of the maxilla. A 55-year-old woman was referred to our department because of pain and swelling in the maxilla.Abstract. Erdheim-Chester disease is an uncommon non-Langerhans cell histiocytosis affecting multiple systems. There is limited knowledge on the imaging capabilities of this disease. We present an extremely rare case of Erdheim-Chester illness in a 67-year-old man with multisystem involvement, including the cardiovascular system, skeleton Erdheim-Chester disease is a rare CD68+, CD1a− non-Langerhans cell histiocytosis with multiorgan involvement. The etiology of Erdheim-Chester disease is unclear; there are no known associated infectious or hereditary genetic abnormalities. However, somatic BRAF mutations have recently been identified in these patients. Historically, the literature regarding the management of Erdheim-Chester |vhd| ytr| xbx| zcx| ssu| pyr| cps| qja| dio| fhl| nhc| fmy| uec| unu| wuw| olm| lww| nyc| jta| idv| mfv| kxy| sau| bef| nsw| mkm| nmy| hna| hpm| bkp| ixq| umv| smv| ujt| qqa| eaf| wxa| aet| jqv| jnw| ump| fiw| kgk| aou| rfv| vuz| nsq| lze| ifa| wta|