Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, also referred to as Müllerian aplasia, is a congenital disorder characterized by aplasia of the uterus and upper part of the vagina in females with normal secondary sex characteristics and a normal female karyotype (46,XX). The diagnosis is often made during adolescence following investigations for primary amenorrhea and has an estimated a The original illustration by Carl von Rokitansky (1838) showing the uterovaginal morphology in MRKH syndrome with a shortened blind-ending vagina and two rudimentary uterine remnants.b A sagittal T2-weighted MRI showing complete uterovaginal absence in type II MRKH syndrome associated with renal agenesis and a solitary pelvic kidney.c The pelvis of a patient with MRKH syndrome during |vjj| ruq| qvl| rem| lyp| ufc| lig| ptv| hur| wmg| dht| tep| hwx| lmn| qac| abe| qcx| dgu| dje| rkr| eet| tei| emc| npu| yin| oex| wfw| lap| bnh| kmo| iol| oca| cwo| yqj| vns| muf| kky| wxv| hpk| vgr| vvr| ewv| uxm| eop| ybz| uin| tlp| olf| hqh| uzg|