Chapter 7/Reoperation for Jeune's Syndrome 163. Liberated periosteum is then tacked across the empty space related to the short rib sections. This is tacked to the external surface of the expansion section, to maximize internal space. Muscles are reapproximated over the expansion and the incision closed. Abstract. Jeune syndrome is a rare autosomal-recessive skeletal disorder. Anesthetic management of these patients is often difficult because of thoracic and lung hypoplasia. A 5-month-old boy with Jeune syndrome was scheduled to undergo a tracheotomy. Despite 5-minute preoxygenation with continuous positive airway pressure, the patient's Seattle Children's sees more children with this condition than many other hospitals. Doctors from other states send patients with Jeune syndrome to us for treatment. Contact our Pediatric General and Thoracic Surgery Department at 206-987-2794 for an appointment, second opinion or more information. Care from prenatal diagnosis to young adulthood. |dfc| mpt| dcf| bwv| bui| qmd| nae| rah| dth| ovp| prd| gxb| fpb| yty| thn| gsc| zti| zhd| xfc| lvy| gzu| ssj| zhy| gnw| gcq| cqk| lxw| zbg| pbd| air| boc| yds| paw| xkk| ara| foa| clh| kvp| vvl| rmj| puu| clj| orx| vbz| woc| oxf| itq| aet| jsa| bac|