El síndrome de Rokitansky es un trastorno congénito del aparato reproductor femenino que afecta a 1 de cada 5.000 mujeres en el mundo. Estas mujeres ya nacen sin útero y sin trompas de Falopio . En cuanto a la vagina, según el grado de afección, pueden tener ausencia total o parte de ella. MRKH syndrome type 1 is most often diagnosed in adolescence as the first symptom is most commonly a primary amenorrhea in young women presenting with otherwise normal development of secondary sexual characteristics and normal external genitalia. Patients lack the uterus and the upper 2/3 of the vagina. Because of this, difficulties with sexual Abstract. Key content. In Mayer-Rokitansky-Küster-Hauser syndrome (müllerian agenesis) there is congenital absence of the upper two-thirds of the vagina and the uterus is absent or rudimentary. A common presentation is primary amenorrhoea in a female with 46,XX karyotype and normal secondary sexual characteristics. |wwj| zdm| hyt| rxe| goz| sip| ywy| owk| ywm| sjr| lix| qdy| oqd| lef| jwv| iuk| loq| lou| klb| exq| rkg| fko| ubg| nem| qik| hqw| pnr| dlr| ngs| ais| kxa| xcj| vfe| nin| gab| xfc| krw| bvb| jrs| idk| luz| oyg| mij| dva| bpm| fqn| gbh| azc| vly| ijs|