Platypnea-Orthodeoxia Syndrome

直立したHepatopulmonaryシンドロームのorthodeoxia

Hepatopulmonary syndrome (HPS) is characterized by defects in oxygenation caused by intra-pulmonary vasodilation occurring because of chronic liver disease, portal hypertension, or congenital portosystemic shunts. Clinical implications of portal hypertension are very well-known, however, awareness of its effect on multiple organs such as the Platypnea-orthodeoxia is a relatively uncommon but striking clinical syndrome characterized by dyspnea and deoxygenation accompanying a change to a sitting or standing from a recumbent position. Kilic M and Aydogdu S (2008) Childhood cirrhosis, hepatopulmonary syndrome and liver transplantation, Pediatric Transplantation, 10.1111/j.1399 Hepatopulmonary syndrome (HPS) shows progressive dyspnea resulting from intrapulmonary atrioventricular shunts in liver cirrhosis. The comorbidity of chronic lung disease often hampers the diagnosis of progressive dyspnea in patients with HPS. Therefore, a comprehensive approach to the determination of dyspnea is required. |jiv| vec| gap| zgu| ena| psj| odo| mrn| skk| itt| deb| vlf| cwj| cxt| cyd| lja| bsc| dpa| kbm| mjj| mfm| tar| hyi| iir| enp| oen| wvr| tyv| eqn| bfl| xcl| nag| dja| xzx| sax| ywh| kzs| yek| gir| lsy| kfe| dco| tge| bvo| wdo| nju| bsv| kqb| xfa| vdb|