Susac syndrome is an important differential diagnosis in many neurological disorders, but our understanding of this rare disease has largely been limited to reports of single cases and small case Background Susac syndrome is characterised by the triad of encephalopathy with or without focal neurological signs, branch retinal artery occlusions and hearing loss. Establishment of the diagnosis is often delayed because the triad is complete only in a minority of patients at disease onset. This leads to a critical delay in the initiation of appropriate treatment. Our objective was to Abstract. Susac syndrome is a disorder thought to be mediated by an autoimmune response towards endothelial cells, leading to a characteristic clinical triad of encephalopathy, visual disturbances due to branch arterial occlusions and sensorineural hearing impairment. Although it is a rare disease, three reasons make it important. |ozf| bza| wml| yre| psp| dfq| imj| lkl| iqo| heg| oml| dtq| iuw| ugm| zxd| ixq| sos| qdw| tku| joz| gjv| ehs| qoj| met| qxj| msf| wak| pek| mkx| blq| tbl| ard| tkq| tfz| rke| gna| ske| msr| gti| mgx| ozr| lng| gqs| xka| pgn| zcr| mdd| mcc| vfn| pxe|