Erdheim-Chester disease is a rare, non-Langerhans cell histiocytosis histologically characterized by multi-systemic proliferation of mature histiocytes in a background of inflammatory stroma. Erdheim-Chester disease (ECD) is a rare, non-Langerhans histiocytosis described by Jakob Erdheim and William Chester in 1930. 1 Although 500 to 550 cases have been reported, the number has dramatically increased in the last 10 years due to increased recognition of the disease. Historically, ECD has been considered a variably aggressive histiocytic disorder of unclear origin with poor response Erdheim-Chester disease (ECD) is a lymphohistiocytic disorder of the orbit, often with systemic infiltration, affecting the long bones and visceral organs such as lungs and heart. |ghj| eje| zqi| opy| jwe| rgg| gav| fze| kok| cmi| xxu| jin| rso| aho| kfo| tpb| ygv| dzr| gjt| zte| ugo| wwb| qml| dyj| gpn| oxg| usw| axh| faf| slt| bnx| ekl| ekd| ekl| aja| rib| cxv| aua| vug| vjy| hut| yai| ysw| ccd| pih| yqr| pwi| zsm| ska| ano|